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Gastroenterology & Hepatology

Hepatic Arteriovenous Malformation (Hereditary HHT)

ICD-10 Code
I78.0_1

Hepatic Arteriovenous Malformation (Hereditary HHT) - Clinical guidelines.

Clinical Presentation & Protocol

Patient Usually Complains Of

Patient presents for follow-up of known Hereditary Hemorrhagic Telangiectasia (HHT) with hepatic involvement. Current symptoms include [asymptomatic / abdominal pain / fatigue / signs of high-output heart failure]. Review of systems negative for gastrointestinal bleeding, jaundice, or encephalopathy. Patient denies recent changes in exercise tolerance or orthopnea.

Clinical Examination Findings

Physical examination reveals [stable / tachycardia / elevated JVP]. Abdominal exam: liver [palpable / non-palpable], presence of [hepatic bruit / hepatomegaly]. Skin exam: presence of mucocutaneous telangiectasias on [lips / tongue / fingertips]. Cardiovascular: [S1/S2 normal / presence of flow murmur]. Extremities: [no edema / peripheral edema].

Treatment Protocol

Management plan: [Observation / Medical therapy with Bevacizumab / Embolization / Liver transplantation evaluation]. Monitor for high-output heart failure and portal hypertension. Continue routine screening for HHT-related vascular malformations. Follow-up imaging scheduled for [date].

Detailed clinical guide coming soon.