Clinical Presentation & Protocol
Patient Usually Complains Of
Patient presents with a congenital midline nasal mass, noted since birth, with associated hypertelorism and widening of the nasal bridge. History of intermittent clear rhinorrhea or pulsatile mass expansion during crying/straining. No history of meningitis or seizures.
Clinical Examination Findings
Physical examination reveals a soft, compressible, non-tender midline nasal mass located at the glabella or nasal dorsum. Positive Furstenberg sign noted. Ocular examination confirms telecanthus and hypertelorism. Nasal endoscopy shows a smooth, mucosa-covered mass protruding into the nasal cavity, potentially obstructing the airway.
Treatment Protocol
Surgical intervention planned via combined neurosurgical and plastic surgery approach. Objectives include intracranial dural repair, excision of the encephalocele sac, and reconstruction of the anterior cranial base defect using autologous bone grafting or synthetic mesh. Nasal reconstruction and aesthetic correction of the nasal dorsum and telecanthus to follow.