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Cardiology / Cardiovascular

PAH - Congenital Heart Associated

ICD-10 Code
I27.89

Comprehensive clinical criteria for PAH - Congenital Heart Associated

Clinical Presentation & Protocol

Patient Usually Complains Of

Patient presents for follow-up of PAH associated with congenital heart disease (CHD). Symptoms include [NYHA Class I/II/III/IV] dyspnea on exertion, fatigue, and occasional palpitations. No reported syncope, chest pain, or peripheral edema. Current CHD anatomy: [e.g., ASD/VSD/PDA/Complex]. Hemodynamics stable on current regimen of [Medication].

Clinical Examination Findings

Vitals: BP [X/X], HR [X], SpO2 [X%]. General: Alert, no acute distress. CV: Regular rate and rhythm, loud P2, holosystolic murmur at [Location], no S3/S4. Lungs: Clear to auscultation bilaterally. Extremities: No cyanosis, no clubbing, trace pedal edema [+/-]. JVP: [Elevated/Normal] cm H2O.

Treatment Protocol

Plan: Continue current PAH-targeted therapy: [Medication/Dose]. Monitor for side effects. Advise strict adherence to sodium-restricted diet. Follow-up with echocardiogram in [Timeframe] to assess RV function and estimated PASP. Repeat 6-minute walk test (6MWT) to evaluate functional capacity.

Detailed clinical guide coming soon.