Clinical Presentation & Protocol
Patient Usually Complains Of
Patient presents with progressive exertional dyspnea and non-productive cough. History significant for recurrent respiratory infections, weight loss, and thoracic discomfort. Note: Evaluate for characteristic "flat-chested" body habitus and history of autoimmune conditions or prior lung transplantation.
Clinical Examination Findings
Physical exam reveals a thin, asthenic body habitus with flattened thoracic cage. Auscultation demonstrates bilateral apical inspiratory crackles. Chest wall inspection may show decreased expansion. Evaluate for signs of chronic hypoxemia, including digital clubbing or cyanosis.
Treatment Protocol
Management plan includes supplemental oxygen for hypoxemia, pulmonary rehabilitation, and nutritional support to address cachexia. Consider immunosuppressive therapy if secondary to autoimmune disease. Monitor for complications including pneumothorax and secondary pulmonary hypertension. Evaluate for lung transplant candidacy.