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Pulmonology / Respiratory

Pulmonary Alveolar Proteinosis (PAP) - Autoimmune

ICD-10 Code
J84.01

Clinical Criteria for Pulmonary Alveolar Proteinosis (PAP) - Autoimmune.

Clinical Presentation & Protocol

Patient Usually Complains Of

Patient presents with progressive exertional dyspnea and non-productive cough. History significant for fatigue and unintentional weight loss. No history of occupational dust exposure or immunosuppression. Symptoms are chronic and insidious in onset.

Clinical Examination Findings

General: Patient appears comfortable at rest, tachypneic on exertion. HEENT: No cyanosis or clubbing noted. Chest: Bilateral fine end-inspiratory crackles (velcro-like) on auscultation. Cardiac: Regular rate and rhythm, no murmurs or peripheral edema.

Treatment Protocol

Plan: Whole Lung Lavage (WLL) scheduled for symptomatic management. Monitor oxygen saturation levels. Consider GM-CSF therapy if refractory. Serial pulmonary function tests (PFTs) and high-resolution CT (HRCT) to monitor disease progression.

Detailed clinical guide coming soon.