Menu
Nephrology & Renal Medicine

Anti-GBM Disease (Goodpasture Syndrome)

ICD-10 Code
M31.0_1

Rare autoimmune disease caused by circulating antibodies against the alpha-3 chain of type IV collagen in the glomerular and alveolar basement membranes. Presents as Rapidly Progressive Glomerulonephritis (RPGN) and diffuse alveolar hemorrhage.

Clinical Presentation & Protocol

Patient Usually Complains Of

Patient presents with a clinical picture highly suggestive of Anti-GBM disease, characterized by rapidly progressive glomerulonephritis (RPGN) and/or pulmonary-renal syndrome. Symptoms include acute onset of hematuria, oliguria, and progressive renal failure, accompanied by dyspnea, cough, and hemoptysis. No history of recent infections or nephrotoxic exposure.

Clinical Examination Findings

Patient appears ill, pale, and tachypneic. Vitals reveal hypertension and tachycardia. Skin exam shows no purpura or rashes. Pulmonary exam reveals bilateral crackles or rhonchi. Edema noted in lower extremities.

Treatment Protocol

Immediate initiation of intensive plasma exchange (PLEX) to remove circulating anti-GBM antibodies. Concurrent immunosuppressive therapy with high-dose intravenous methylprednisolone followed by oral prednisone and cyclophosphamide. Monitor renal function and hemoglobin levels closely.

Detailed clinical guide coming soon.