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gastrointestinal

Congenital Hepatic Fibrosis

ICD-10 Code
Q44.6_2

Congenital Hepatic Fibrosis - Clinical guidelines.

Clinical Presentation & Protocol

Patient Usually Complains Of

Autosomal recessive disorder with portal hypertension and preserved synthetic function.

Clinical Examination Findings

Exam depends on severity.

Treatment Protocol

Treat underlying cause, supportive care.

Detailed clinical guide coming soon.