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Pulmonology / Respiratory

Hughes-Stovin Syndrome

ICD-10 Code
M31.8

Clinical Criteria for Hughes-Stovin Syndrome.

Clinical Presentation & Protocol

Patient Usually Complains Of

Patient presents with a history of recurrent thrombophlebitis and progressive pulmonary artery aneurysms. Symptoms include hemoptysis, dyspnea, and persistent cough. No evidence of active Behรงetโ€™s disease manifestations currently noted. Review of systems positive for intermittent fever and malaise.

Clinical Examination Findings

Physical examination reveals stable vital signs with mild tachycardia. Pulmonary auscultation demonstrates decreased breath sounds in affected areas. Cardiovascular exam shows no murmurs, though peripheral venous assessment is positive for signs of superficial thrombophlebitis. Skin exam negative for active oral or genital ulcerations.

Treatment Protocol

Initiate immunosuppressive therapy with high-dose corticosteroids and cyclophosphamide to manage vasculitic progression. Anticoagulation is contraindicated due to the high risk of pulmonary artery aneurysm rupture. Surgical consultation requested for potential endovascular intervention or resection of symptomatic aneurysms.

Detailed clinical guide coming soon.